A rhabdomyoma in the right ventricle presenting as hemodynamics of hypoplastic right heart

Daiji Takajo, Sanjeev Aggarwal

Research output: Contribution to journalArticlepeer-review

Abstract

Rhabdomyomas are the most common paediatric cardiac tumours. The natural history of these tumours is mostly benign, and the tumour usually regresses spontaneously. Although surgical resection of these tumours is one of the considerations in patients with ventricular outflow obstruction, a palliation with Blalock-Taussig shunt is an alternative approach with the hope of regression of the tumour over time. We report a case of prenatally diagnosed rhabdomyomas in the right ventricle and its outflow presenting as hemodynamic simulating hypoplastic right ventricle in a newborn. She required prostaglandin and Blalock-Taussig shunts palliation for pulmonary flow and subsequent regression of tumours.

Original languageEnglish
Pages (from-to)1527-1529
Number of pages3
JournalCardiology in the Young
Volume30
Issue number10
DOIs
StatePublished - Oct 2020

Keywords

  • Blalock-Taussig shunt
  • Rhabdomyomas
  • hypoplastic right ventricle physiology

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