TY - JOUR
T1 - Diagnosis and Management of the Unligated Vertical Vein in Repaired Total Anomalous Pulmonary Venous Connection
AU - Akam-Venkata, Jyothsna
AU - Turner, Daniel R.
AU - Joshi, Aparna
AU - Aggarwal, Sanjeev
AU - Gupta, Pooja
N1 - Publisher Copyright:
© The Author(s) 2019.
PY - 2020/7/1
Y1 - 2020/7/1
N2 - During initial repair of supracardiac total anomalous pulmonary venous connection (TAPVC), the vertical vein (VV) is sometimes left patent (not ligated or divided) in the hope that this strategy may reduce the likelihood or severity of postoperative pulmonary hypertensive crises. We report a case of a 35-year-old pregnant patient with previously repaired supracardiac TAPVC who presented with atrial arrhythmia and right heart dilation. A cardiac magnetic resonance imaging study confirmed the diagnosis of patency of the vertical vein and right heart dilation. The VV was occluded with a catheter-delivered vascular occlusion device through a percutaneous approach, resulting in resolution of right heart dilation and arrhythmia. This case highlights the role of cross-sectional imaging as an adjunct to echocardiography in adults with repaired congenital heart disease.
AB - During initial repair of supracardiac total anomalous pulmonary venous connection (TAPVC), the vertical vein (VV) is sometimes left patent (not ligated or divided) in the hope that this strategy may reduce the likelihood or severity of postoperative pulmonary hypertensive crises. We report a case of a 35-year-old pregnant patient with previously repaired supracardiac TAPVC who presented with atrial arrhythmia and right heart dilation. A cardiac magnetic resonance imaging study confirmed the diagnosis of patency of the vertical vein and right heart dilation. The VV was occluded with a catheter-delivered vascular occlusion device through a percutaneous approach, resulting in resolution of right heart dilation and arrhythmia. This case highlights the role of cross-sectional imaging as an adjunct to echocardiography in adults with repaired congenital heart disease.
KW - adult congenital heart disease
KW - cardiac MRI
KW - total anomalous pulmonary venous connection
KW - unligated vertical vein
UR - http://www.scopus.com/inward/record.url?scp=85147465051&partnerID=8YFLogxK
U2 - 10.1177/2150135118817491
DO - 10.1177/2150135118817491
M3 - Article
C2 - 30983537
AN - SCOPUS:85147465051
SN - 2150-1351
VL - 11
SP - NP229-NP231
JO - World Journal for Pediatric and Congenital Heart Surgery
JF - World Journal for Pediatric and Congenital Heart Surgery
IS - 4
ER -