TY - JOUR
T1 - Surgical and medical results of complete atrioventricular canal
T2 - A ten year review
AU - Clapp, Sandra K.
AU - Perry, Burton L.
AU - Farooki, Zia Q.
AU - Jackson, William L.
AU - Karpawich, Peter P.
AU - Hakimi, Medhi
AU - Arciniegas, Eduardo
AU - Green, Edward W.
PY - 1987/2/15
Y1 - 1987/2/15
N2 - The files of 121 patients who presented to Children's Hospital of Michigan over the last 10 years with complete atrioventricular (AV) canal were reviewed to evaluate long-term management and overall outcome. Of 121 patients, 70 underwent corrective surgery, 21 (30%) of whom died perioperatively. The surgical mortality rate was 13% when patients with hypoplastic left or right ventricle (n = 6), double-orifice mitral valve or extreme deficiency of mitral tissue (n = 5), and pulmonary vascular obstructive disease (n = 5) were excluded. Of the 49 patients who survived operation, 36 are in New York Heart Association class I, 1 patient requires a pacemaker and 3 died late. In 34 of the 51 patients (28%) who did not undergo operation, pulmonary vascular obstructive disease developed; it occurred within 12 months in 10 patients (8%). Eight other patients who did not undergo operation died before planned surgery (age 1 to 9 months). Although surgical prognosis in good candidates is acceptable, the overall prognosis for children with complete AV canal is guarded because of the risk of early death or early pulmonary vascular obstructive disease and frequently unfavorable anatomy.
AB - The files of 121 patients who presented to Children's Hospital of Michigan over the last 10 years with complete atrioventricular (AV) canal were reviewed to evaluate long-term management and overall outcome. Of 121 patients, 70 underwent corrective surgery, 21 (30%) of whom died perioperatively. The surgical mortality rate was 13% when patients with hypoplastic left or right ventricle (n = 6), double-orifice mitral valve or extreme deficiency of mitral tissue (n = 5), and pulmonary vascular obstructive disease (n = 5) were excluded. Of the 49 patients who survived operation, 36 are in New York Heart Association class I, 1 patient requires a pacemaker and 3 died late. In 34 of the 51 patients (28%) who did not undergo operation, pulmonary vascular obstructive disease developed; it occurred within 12 months in 10 patients (8%). Eight other patients who did not undergo operation died before planned surgery (age 1 to 9 months). Although surgical prognosis in good candidates is acceptable, the overall prognosis for children with complete AV canal is guarded because of the risk of early death or early pulmonary vascular obstructive disease and frequently unfavorable anatomy.
UR - http://www.scopus.com/inward/record.url?scp=0023157887&partnerID=8YFLogxK
U2 - 10.1016/0002-9149(87)90955-6
DO - 10.1016/0002-9149(87)90955-6
M3 - Article
C2 - 3812315
AN - SCOPUS:0023157887
VL - 59
SP - 454
EP - 458
JO - The American Journal of Cardiology
JF - The American Journal of Cardiology
SN - 0002-9149
IS - 5
ER -